WARNING: This product is for research use only, not for human or veterinary use.
MedKoo CAT#: 597158
Description: N-Isovalerylglutamic acid belongs to the class of organic compounds known as glutamic acid and derivatives. These are compounds containing glutamic acid or a derivative thereof resulting from reaction of glutamic acid at the amino group or the carboxy group, or from the replacement of any hydrogen of glycine by a heteroatom.
MedKoo Cat#: 597158
Name: N-Isovalerylglutamic acid
Chemical Formula: C10H17NO5
Exact Mass: 231.1107
Molecular Weight: 231.24
Elemental Analysis: C, 51.94; H, 7.41; N, 6.06; O, 34.59
Synonym: N-Isovalerylglutamic acid; N-Ivga;
IUPAC/Chemical Name: (3-methylbutanoyl)-L-glutamic acid
InChi Key: HCVIJONZMYVLAW-ZETCQYMHSA-N
InChi Code: InChI=1S/C10H17NO5/c1-6(2)5-8(12)11-7(10(15)16)3-4-9(13)14/h6-7H,3-5H2,1-2H3,(H,11,12)(H,13,14)(H,15,16)/t7-/m0/s1
SMILES Code: O=C(O)CC[C@@H](C(O)=O)NC(CC(C)C)=O
1: Niederwieser A, Steinmann B, Exner U, Neuheiser F, Redweik U, Wang M, Rampini S, Wendel U. Multiple acyl-Co A dehydrogenation deficiency (MADD) in a boy with nonketotic hypoglycemia, hepatomegaly, muscle hypotonia and cardiomyopathy. Detection of N-isovalerylglutamic acid and its monoamide. Helv Paediatr Acta. 1983 Mar;38(1):9-26. PubMed PMID: 6862997.
2: Lehnert W. Excretion of N-isovalerylglutamic acid in isovaleric acidemia. Clin Chim Acta. 1981 Oct 26;116(2):249-52. PubMed PMID: 7296890.